源于大网膜的恶性肾外横纹肌样瘤：病例报告及文献复习。
Malignant Extrarenal Rhabdoid tumor derived from the greater omentum: A case report and literature review.
机构信息
School of Medical and Life Science, Chengdu University of Traditional Chinese Medicine, Chengdu, China.
Department of Gynecology, Suining Central Hospital, Suining, China.
出版信息
Cancer Rep (Hoboken). 2024 May;7(5):e2086. doi: 10.1002/cnr2.2086.
BACKGROUND
Malignant extrarenal rhabdoid tumor (MERT) is a rare and highly metastatic tumor, which is more than 75% of patients dying within 6 months of initial diagnosis, and it often leads to misdiagnosis and delayed treatment.
CASE
This paper reports a 16-year-old girl who presented with the chief complaint of acute abdominal pain. She underwent laparoscopic exploration and excisional biopsy, then pathological examination and immunohistochemistry revealed "extrarenal malignant rhabdomyoma." One month after operation, she died of intra-abdominal hemorrhage and multiple organ dysfunction.
CONCLUSION
MERT were often misdiagnosed and had a poor prognosis. The surgery and chemotherapy are usually beneficial to prolong the survival time of patients with MERT.
背景
恶性肾外横纹肌样瘤（MERT）是一种罕见且高度转移性的肿瘤，超过 75%的患者在初始诊断后 6 个月内死亡，常导致误诊和治疗延误。
病例报告
本文报道了 1 例 16 岁女性，因腹痛就诊。行腹腔镜探查术和切除活检，然后行病理检查和免疫组化检查提示“肾外恶性横纹肌样瘤”。术后 1 个月，因腹腔内出血和多器官功能衰竭死亡。
结论
MERT 常被误诊，预后不良。手术和化疗通常有利于延长 MERT 患者的生存时间。
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