Neurosurgery Department, University Hospital of Caen, France.
Radiology Pediatric Department, University Hospital of Caen, France.
Neurochirurgie. 2024 Sep;70(5):101571. doi: 10.1016/j.neuchi.2024.101571. Epub 2024 May 30.
Anterior sacral meningocele is a rare congenital disorder, occurring isolated or in syndromic disease.
A 15-year-old patient who complained of abdominal pain and urinary dysfunction was managed surgically. Imaging diagnosed a giant presacral meningocele and agenesis of the coccyx.
The presentation of sacral meningocele can be poorly symptomatic, which is why some patients are diagnosed late. Sometimes, diagnosis is suggested by non-specific abdominal symptoms or complications. Abdominal-pelvic radiological examination and lumbar spine MRI are essential, and treatment must be surgical. There are several surgical approaches, but currently no consensus.
An unusual huge presacral cystic mass in a young patient may be isolated or part of a syndrome, and can be asymptomatic for a long time, leading to late diagnosis. The surgical approach should be based on multidisciplinary discussion. We operated on a giant anterior sacral meningocele in a child using a posterior approach, with a satisfactory result.
前骶膜膨出是一种罕见的先天性疾病,可单独发生或与综合征相关。
一名 15 岁的患者,主诉腹痛和排尿功能障碍,接受了手术治疗。影像学诊断为巨大的骶前脊膜膨出和尾骨发育不全。
骶膜膨出的表现可能症状不明显,这就是为什么有些患者诊断较晚。有时,非特异性的腹部症状或并发症提示诊断。腹部-骨盆放射学检查和腰椎 MRI 是必要的,治疗必须是手术。有几种手术方法,但目前尚无共识。
年轻患者出现异常巨大的骶前囊性肿块可能是孤立的或综合征的一部分,并且可能长时间无症状,导致诊断延迟。手术方法应基于多学科讨论。我们对一名儿童采用后路手术治疗巨大的前骶膜膨出,效果满意。