Department of Endocrinology and Diabetes, Toyohashi Municipal Hospital, Aichi 441-8570, Japan.
Department of Internal Medicine, Atsumi Hospital, Aichi 441-3415, Japan.
Endocr J. 2024 Oct 1;71(10):1003-1011. doi: 10.1507/endocrj.EJ23-0725. Epub 2024 Jul 10.
A 38-year-old Japanese woman with a history of abnormal thyroid function of non-autoimmune origin, pituitary endocrine tumor, and untreated diabetes mellitus was referred to our outpatient clinic when she became pregnant with twins. Physical findings consistent with Cushing's syndrome (CS) were absent at the time of presentation. Although baseline plasma adrenocorticotropic hormone, serum cortisol, and 24-hour urinary free cortisol excretion levels were above the upper limits of normal non-pregnant reference ranges, we could not exclude a physiological increase associated with pregnancy. No medical or surgical intervention for hypercortisolism was performed during pregnancy. Spontaneous vaginal delivery resulted in the normal delivery of live twins. A diagnosis of Cushing's disease (CD) was established when papery skin developed postpartum. Transsphenoidal surgery was performed and the hypercortisolism partially resolved post-operatively. The patient's abnormal thyroid function also resolved. Pregnancy in women with endogenous CS is rare, with less than 300 cases reported. Most reported cases of CS during pregnancy are of adrenal origin. Only two cases of twin pregnancies with CD have been reported. Therefore, we reported the third case of CD in a twin pregnancy and reviewed the diagnostic and therapeutic challenges associated with CD during pregnancy.
一位 38 岁的日本女性,有非自身免疫性起源的甲状腺功能异常、垂体内分泌肿瘤和未经治疗的糖尿病病史,在怀上双胞胎时被转介到我们的门诊。就诊时,她没有出现库欣综合征(CS)的典型体征。尽管基础血浆促肾上腺皮质激素、血清皮质醇和 24 小时尿游离皮质醇排泄水平高于正常非妊娠参考范围的上限,但我们不能排除与妊娠相关的生理性升高。在妊娠期间,未对皮质醇增多症进行任何药物或手术干预。自发性阴道分娩导致双胞胎正常分娩。产后出现纸样皮肤,诊断为库欣病(CD)。进行了经蝶窦手术,术后高皮质醇血症部分缓解。患者的异常甲状腺功能也得到了缓解。内源性 CS 患者的妊娠很少见,报道的病例不到 300 例。大多数报道的妊娠期间 CS 为肾上腺来源。仅报道了两例 CD 双胞胎妊娠。因此,我们报告了第三例 CD 双胞胎妊娠,并回顾了与妊娠期间 CD 相关的诊断和治疗挑战。