Callahan Ryan, Morray Brian H, Hirsch Russel, Petit Christopher J
Department of Cardiology, Boston Children's Hospital and Harvard Medical School, Boston, Massachusetts.
Division of Pediatric Cardiology, Seattle Children's Hospital and University of Washington School of Medicine, Seattle, Washington.
J Soc Cardiovasc Angiogr Interv. 2022 Jun 30;1(5):100391. doi: 10.1016/j.jscai.2022.100391. eCollection 2022 Sep-Oct.
Pediatric intraluminal pulmonary vein stenosis has evolved into a chronic illness, with improving survival. Although significant knowledge gaps remain, medical providers have found success in the management of patients with pulmonary vein stenosis using a comprehensive multimodality treatment strategy. This review discusses the core principles employed by 4 centers dedicated to improving pulmonary vein stenosis outcomes, including how to make the diagnosis, educating the family, treatment strategy, the importance of surveillance, and the management of symptoms and comorbidities.
小儿管腔内肺静脉狭窄已演变成一种慢性病，生存率不断提高。尽管仍存在重大的知识空白，但医疗服务提供者已成功地采用综合多模式治疗策略来管理肺静脉狭窄患者。本综述讨论了4个致力于改善肺静脉狭窄治疗结果的中心所采用的核心原则，包括如何进行诊断、对家属进行教育、治疗策略、监测的重要性以及症状和合并症的管理。
