Department of Ophthalmology, Dokkyo Medical University Hospital, Tochigi, Japan.
Medicine (Baltimore). 2024 Aug 16;103(33):e39359. doi: 10.1097/MD.0000000000039359.
Lifebuoy cataract is a rare congenital condition characterized by lens thinning. Due to its rarity, detailed treatment reports and standardized surgical approaches are limited. This study aims to enhance the current body of knowledge by presenting comprehensive case reports and describing surgical techniques for the treatment of lifebuoy cataracts.
A 14-year-old boy was diagnosed with a congenital cataract in his right eye at the age of 9, which was left untreated. The patient visited our hospital due to progressive visual impairment.
The visual acuity of the right eye was counting fingers at 30 cm. The uncorrected visual acuity of the left eye was 20/100, whereas the best corrected visual acuity was 20/20. The intraocular pressures were 18 mm Hg (left eye) and 20 mm Hg (right eye). Slit-lamp microscopy revealed central calcification of the lens capsule in the right eye and slightly opaque cortical tissue in the periphery, with no observable lens nucleus. Anterior segment optical coherence tomography (CASIA2, TOMEY, Nagoya, Japan) of the right eye showed fused anterior and posterior capsules and an absence of the lens nucleus, leading to a diagnosis of lifebuoy cataract.
Cataract surgery was performed on the right eye. Following a 2.4-mm sclerocorneal incision and trypan blue staining, continuous curvilinear capsulorrhexis was performed around the central opacity. The surrounding cortex was removed using irrigation and aspiration, while a viscoelastic agent was injected between the central calcified membrane and the posterior capsule. The membranous tissue was carefully peeled away and removed using forceps. Despite residual posterior capsular opacification, posterior capsulotomy was not performed due to concerns about vitreous prolapse. The intraocular lens was fixed within the capsule. Ten days post-surgery, the remaining posterior capsular opacification was treated with neodymium-doped yttrium aluminum garnet laser capsulotomy.
The uncorrected visual acuity and best corrected visual acuity of the right eye improved to 20/100 and 20/50, respectively.
This case report demonstrates a successful surgical approach for a lifebuoy cataract, highlighting its unique morphology and the need for careful, specialized techniques. These findings aim to guide ophthalmologists in managing this rare condition, potentially improving patient care.
救生圈白内障是一种罕见的先天性晶状体变薄疾病。由于其罕见性,详细的治疗报告和标准化的手术方法有限。本研究旨在通过提供全面的病例报告并描述救生圈白内障的治疗手术技术,来丰富现有知识体系。
一名 14 岁男孩,9 岁时被诊断出右眼患有先天性白内障,未接受治疗。因视力逐渐下降,患者来我院就诊。
右眼视力手动 30cm,左眼未矫正视力 20/100,最佳矫正视力 20/20,双眼眼压分别为 18mmHg(左眼)和 20mmHg(右眼)。裂隙灯显微镜检查显示右眼晶状体囊中央钙化,周边皮质组织略混浊,未见晶状体核。右眼眼前节光学相干断层扫描(CASIA2,TOMEY,名古屋,日本)显示前囊和后囊融合,晶状体核缺失,诊断为救生圈白内障。
右眼行白内障手术。2.4mm 巩膜角膜切口,三苯甲烷蓝染色后行中央混浊部连续环形撕囊。用灌洗抽吸法清除周边皮质,在前囊中央钙化膜与后囊之间注入黏弹剂,小心剥除膜性组织并用镊子取出。尽管后囊仍混浊,但因担心玻璃体脱出,未行后囊切开术。将人工晶状体固定在囊袋内。术后 10 天,行钕掺杂钇铝石榴石激光后囊切开术治疗残余后囊混浊。
右眼未矫正视力和最佳矫正视力分别提高至 20/100 和 20/50。
本病例报告展示了救生圈白内障的成功手术方法,突出了其独特的形态,并强调需要采用精细、专业的技术。这些发现旨在为眼科医生管理这种罕见疾病提供指导,有望改善患者的治疗效果。