Karjala Sri Lasya, Namala Satya Prasad, Machiraju Phani Krishna, Pandurangan Prabu
Department of General Medicine, Apollo Hospitals, Chennai 600 006, Tamilnadu, India.
Department of Hematology, Apollo Hospitals, Chennai 600 006, Tamilnadu, India.
Oxf Med Case Reports. 2024 Sep 7;2024(9):omae102. doi: 10.1093/omcr/omae102. eCollection 2024 Sep.
Good's syndrome (GS) is a rare adult-onset thymoma associated with acquired combined B-cell and T-cell immunodeficiency. It has similarities with Common variable immunodeficiency (CVID) in terms of hypogammaglobulinemia and significant risk of invasive bacterial and opportunistic infections. We still have a long way to go in understanding the pathogenesis of Good's syndrome. Here, we describe a case of a middle-aged female with thymoma and recurrent opportunistic infections. Clinico-laboratory evaluation led to a diagnosis of GS and she showed good response to intravenous immunoglobulin. Clinicians should be aware that thymoma can precede the onset of immunodeficiency.
古德综合征(GS)是一种罕见的成人起病的胸腺瘤,与获得性B细胞和T细胞联合免疫缺陷相关。在低丙种球蛋白血症以及侵袭性细菌感染和机会性感染的显著风险方面,它与普通可变免疫缺陷(CVID)有相似之处。我们在理解古德综合征的发病机制方面仍有很长的路要走。在此,我们描述一例患有胸腺瘤和复发性机会性感染的中年女性病例。临床实验室评估确诊为GS,她对静脉注射免疫球蛋白显示出良好反应。临床医生应意识到胸腺瘤可能先于免疫缺陷发作。