Lahnine Ghita, Saddouki Fatima, Bouanani Zineb, Akammar Amal, Bouardi Nizar El, Haloua Meriem, Alami Badr, Lamrani Youssef A, Maaroufi Mustapha, Boubbou Meriem
Mother and Child Radiology Department, University of Sidi Mohammed Benabdellah, CHU Hassan II, Fes, Morocco.
Central Radiology Department, University of Sidi Mohammed Benabdellah, CHU Hassan II, Fes, Morocco.
Radiol Case Rep. 2024 Aug 24;19(11):5196-5200. doi: 10.1016/j.radcr.2024.07.146. eCollection 2024 Nov.
A rare disorder called congenital infiltrating lipomatosis of the face is characterized by a diffuse fatty infiltration of the soft tissues of the face. Muscle involvement and related bony hyperplasia may coexist. This particular form of lipomatous tumor is rare and typically appears in childhood. It is congenital in nature. Collections of mature, nonencapsulated lipocytes that infiltrate local tissues and frequently recur following surgery define congenital infiltrating lipomatosis, a unique clinicopathologic condition. The best modalities are, CT scan and MRI since they can determine the extent of the lesions and reveal their fat content. The treatment of this disease is surgical as soon as possible to restrict their infiltrative growth and improve the appearance of the face. We describe a case of massive facial invading lipoma that was investigated using MRI.
一种名为先天性面部浸润性脂肪瘤病的罕见疾病,其特征为面部软组织的弥漫性脂肪浸润。可能并存肌肉受累及相关骨质增生。这种特殊类型的脂肪瘤性肿瘤罕见,通常在儿童期出现,本质上是先天性的。成熟的、无包膜的脂肪细胞聚集浸润局部组织且术后常复发,这界定了先天性浸润性脂肪瘤病,一种独特的临床病理状况。最佳的检查方式是CT扫描和MRI,因为它们能确定病变范围并显示其脂肪含量。本病的治疗应尽早手术,以限制其浸润性生长并改善面部外观。我们描述了一例使用MRI检查的巨大面部侵袭性脂肪瘤病例。