支气管闭锁伴艾森曼格综合征在复杂先天性心脏病中的罕见共存：一例报告。

Bronchial Atresia with Eisenmenger Syndrome in a Complex Congenital Heart Disease-A Rare Coexistence: A Case Report.

机构信息

Assistant Professor, Department of Radiodiagnosis, Indira Gandhi Medical College & Hospital, Shimla, Himachal Pradesh, India, Corresponding Author.

Associate Professor, Department of Radiodiagnosis, Indira Gandhi Medical College & Hospital, Shimla, Himachal Pradesh, India.

出版信息

J Assoc Physicians India. 2024 Oct;72(10):e31-e33. doi: 10.59556/japi.72.0693.

DOI:10.59556/japi.72.0693

PMID:39390879

Abstract

BACKGROUND

Congenital bronchial atresia (CBA) is a relatively benign and uncommon pulmonary anomaly that is usually an incidental radiological finding. Bronchial atresia may also be acquired. Its association with pulmonary vascular anomalies and congenital heart disease (CHD) has been described in literature as a handful of case reports only.

CASE DESCRIPTION

We report a case of a 26-year-old female having a rare coexistence of bronchial atresia with a large patent ductus arteriosus (PDA) and a small atrial septal defect (ASD), and had Eisenmenger syndrome (ES) at the time of presentation. PDA itself causes pulmonary arterial hypertension (PAH) if not corrected early within a few months of infancy. On the contrary, CBA can also lead to PAH and along with PDA may have contributed to the development of ES in our case.

CONCLUSION

Timely diagnosis and treatment of CBA and its associated CHD may prevent or delay the complications occurring later on.

摘要

背景

先天性支气管闭锁（CBA）是一种相对良性且不常见的肺部异常，通常是偶然发现的影像学结果。支气管闭锁也可能是后天获得的。其与肺血管异常和先天性心脏病（CHD）的关联仅在少数病例报告中有所描述。

病例描述

我们报告了一例 26 岁女性罕见共存支气管闭锁、大型动脉导管未闭（PDA）和小房间隔缺损（ASD），并在就诊时患有艾森曼格综合征（ES）。如果不及时在婴儿期后几个月内纠正，PDA 本身会导致肺动脉高压（PAH）。相反，CBA 也可能导致 PAH，并且与 PDA 一起可能导致我们病例中 ES 的发生。