Sanford R A, Smith R A
J Neurosurg. 1986 Feb;64(2):317-21. doi: 10.3171/jns.1986.64.2.0317.
Solid hemangioblastomas of the cervicomedullary junction are benign vascular neoplasms malignantly located. Their unusual and characteristic clinical presentations include loss of involuntary respiratory drive, neurogenic hypertension, and emesis; these are secondary to their involvement of the tractus solitarius in the medulla. Although angiography is diagnostic, the computerized tomography appearance and unusual location also suggest the diagnosis. The correct preoperative diagnosis is particularly important for the successful surgical excision of these vascular tumors. The microsurgical removal of cervicomedullary hemangioblastomas is described in three patients.
延髓颈髓交界处的实性血管母细胞瘤是恶性定位的良性血管肿瘤。其不寻常且具有特征性的临床表现包括自主呼吸驱动丧失、神经源性高血压和呕吐;这些是由于它们累及延髓的孤束所致。尽管血管造影具有诊断性,但计算机断层扫描表现和不寻常的位置也提示了诊断。正确的术前诊断对于成功手术切除这些血管肿瘤尤为重要。本文描述了3例患者延髓颈髓血管母细胞瘤的显微手术切除情况。