Shan Ning, Shang Yu, He Yaowu, Wen Zhe, Ning Shangwei, Chen Hong
Harbin Medical University, Harbin, Heilongjiang Province, China.
Department of Pulmonary and Critical Care Medicine, The Second Affiliated Hospital of Harbin Medical University, Harbin, Heilongjiang Province, China.
Sci Rep. 2025 Jan 3;15(1):610. doi: 10.1038/s41598-024-84820-3.
Interstitial lung disease (ILD) is known to be a major complication of systemic sclerosis (SSc) and a leading cause of death in SSc patients. As the most common type of ILD, the pathogenesis of idiopathic pulmonary fibrosis (IPF) has not been fully elucidated. In this study, weighted correlation network analysis (WGCNA), protein‒protein interaction, Kaplan-Meier curve, univariate Cox analysis and machine learning methods were used on datasets from the Gene Expression Omnibus database. CCL2 was identified as a common characteristic gene of IPF and SSc. The genes associated with CCL2 expression in both diseases were enriched mainly in chemokine-related pathways and lipid metabolism-related pathways according to Gene Set Enrichment Analysis. Single-cell RNA sequencing (sc-RNAseq) revealed a significant difference in CCL2 expression in alveolar epithelial type 1/2 cells, mast cells, ciliated cells, club cells, fibroblasts, M1/M2 macrophages, monocytes and plasma cells between IPF patients and healthy donors. Statistical analyses revealed that CCL2 was negatively correlated with lung function in IPF patients and decreased after mycophenolate mofetil (MMF) treatment in SSc patients. Finally, we identified CCL2 as a common biomarker from IPF and SSc, revealing the common mechanism of these two diseases and providing clues for the study of the treatment and mechanism of these two diseases.
间质性肺疾病(ILD)是系统性硬化症(SSc)的主要并发症,也是SSc患者的主要死因。作为最常见的ILD类型,特发性肺纤维化(IPF)的发病机制尚未完全阐明。在本研究中,对来自基因表达综合数据库的数据集使用了加权基因共表达网络分析(WGCNA)、蛋白质-蛋白质相互作用、Kaplan-Meier曲线、单变量Cox分析和机器学习方法。CCL2被确定为IPF和SSc的共同特征基因。根据基因集富集分析,在这两种疾病中与CCL2表达相关的基因主要富集于趋化因子相关途径和脂质代谢相关途径。单细胞RNA测序(sc-RNAseq)显示,IPF患者与健康供体相比,肺泡1型/2型上皮细胞、肥大细胞、纤毛细胞、棒状细胞、成纤维细胞、M1/M2巨噬细胞、单核细胞和浆细胞中CCL2表达存在显著差异。统计分析显示,CCL2与IPF患者的肺功能呈负相关,且在SSc患者接受霉酚酸酯(MMF)治疗后降低。最后,我们确定CCL2为IPF和SSc的共同生物标志物,揭示了这两种疾病的共同机制,并为这两种疾病的治疗和机制研究提供了线索。