Afonso Rita, Calças Marques Roberto, Viana Helena, Cabrita Ana, Paula Silva Ana
Nephrology Department, Unidade Local de Saúde (ULS) Algarve - Hospital de Faro, Faro, PRT.
Nephrology Department, Unidade Local de Saúde (ULS) São José - Hospital Curry Cabral, Lisbon, PRT.
Cureus. 2024 Dec 14;16(12):e75701. doi: 10.7759/cureus.75701. eCollection 2024 Dec.
Fibrillary glomerulonephritis (FGN) is a rare glomerular disease characterized by the deposition of fibrils within the mesangium and glomerular basement membrane. Most cases are idiopathic, but it can be linked to autoimmune diseases, neoplasms, and infections. There is limited evidence on the best treatment approach, and many patients progress to end-stage kidney disease. The authors present a case of FGN in a patient with Sjögren's syndrome (SS) and primary biliary cholangitis (PBC), highlighting a successful clinical outcome.
纤维性肾小球肾炎(FGN)是一种罕见的肾小球疾病,其特征是在系膜和肾小球基底膜内有纤维沉积。大多数病例为特发性,但也可能与自身免疫性疾病、肿瘤和感染有关。关于最佳治疗方法的证据有限,许多患者会发展为终末期肾病。作者报告了一例患有干燥综合征(SS)和原发性胆汁性胆管炎(PBC)的FGN患者,并强调了成功的临床结果。