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电视辅助胸腔镜肺叶切除术治疗罕见部分性肺静脉异位连接患者:病例报告

Video-assisted thoracoscopic lobectomy for a patient with rare partial anomalous pulmonary vein connection: Case report.

作者信息

Yibulayin Xiayimaierdan, Feida Guliniaer, Sun Xiaohong

机构信息

Department of Thoracic Surgery, Affiliated Tumor Hospital of Xinjiang Medical University, Urumqi, China.

Department of Radiology, Affiliated Tumor Hospital of Xinjiang Medical University, Urumqi, China.

出版信息

Medicine (Baltimore). 2025 May 9;104(19):e42461. doi: 10.1097/MD.0000000000042461.

DOI:10.1097/MD.0000000000042461
PMID:40355182
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12074068/
Abstract

RATIONALE

Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital vascular anomaly that often remains undetected in asymptomatic patients. While most cases are hemodynamically insignificant, failure to recognize PAPVC preoperatively may lead to intraoperative misidentification and surgical complications. Coexistence of PAPVC and lung cancer, particularly on the ipsilateral side, is extremely rare and poses challenges for surgical decision-making.

PATIENT CONCERNS

A 55-year-old man, asymptomatic and uncharacteristic in his past medical history, presented with an abnormal shadow in the left lower lobe during a regular checkup.

DIAGNOSES

Pulmonary sarcomatoid carcinoma, partial anomalous pulmonary vein connection.

INTERVENTIONS

The patient underwent video-assisted thoracoscopic left lower lobectomy without surgical correction of the PAPVC.

OUTCOMES

The patient remained in good health at the 14-month follow-up.

LESSONS

In patients with ipsilateral PAPVC and no evidence of hemodynamic compromise, anatomical lobectomy alone may be a safe and effective surgical option without the need for venous correction.

摘要

理论依据

部分性肺静脉异位连接(PAPVC)是一种罕见的先天性血管异常,在无症状患者中常未被发现。虽然大多数病例在血流动力学上无显著意义,但术前未识别PAPVC可能导致术中误认及手术并发症。PAPVC与肺癌并存,尤其是同侧并存,极为罕见,给手术决策带来挑战。

患者情况

一名55岁男性,无症状且既往病史无特殊,在定期体检时发现左肺下叶有异常阴影。

诊断

肺肉瘤样癌,部分性肺静脉异位连接。

干预措施

患者接受了电视辅助胸腔镜下左肺下叶切除术,未对PAPVC进行手术矫正。

结果

在14个月的随访中,患者健康状况良好。

经验教训

对于同侧PAPVC且无血流动力学受损证据的患者,单纯解剖性肺叶切除术可能是一种安全有效的手术选择,无需进行静脉矫正。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/f8871f2c5721/medi-104-e42461-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/05b4679a2f79/medi-104-e42461-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/f00b47b5f5d0/medi-104-e42461-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/fd12b6b23180/medi-104-e42461-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/f8871f2c5721/medi-104-e42461-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/05b4679a2f79/medi-104-e42461-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/f00b47b5f5d0/medi-104-e42461-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/fd12b6b23180/medi-104-e42461-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b674/12074068/f8871f2c5721/medi-104-e42461-g004.jpg

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Partial Anomalous Pulmonary Venous Return in Adults.成人部分性肺静脉异位回流
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