Use of mixed dispersion of fluorescent galactosylceramide and sodium dodecylsulfate for assaying galactosylceramide-beta-galactosidase and diagnosing Krabbe disease.
作者信息
Salvayre R, Gatt S
出版信息
Enzyme. 1985;33(3):175-80. doi: 10.1159/000469429.
PMID:4054076
Abstract
A fluorescent derivative of galactosylceramide [NBD-GalCer: 12-N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl)aminodecanoyl+ ++ galactosylceramide] was dispersed in sodium dodecylsulfate and used to determine the activity of galactosylceramide-beta-galactosidase. Optimal assay conditions were defined, compared to other assay procedures and found suitable for diagnosing Krabbe disease.
摘要
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