Pech A, Cannoni M, Triglia J M, Zanaret M, Thomassin J M
Ann Otolaryngol Chir Cervicofac. 1985;102(7):525-30.
Among the various congenital cervicofacial swellings observed in children, three types are rarely encountered in general practice: auriculobranchial cysts and fistulae, thymic cysts and cystic lymphangiomas. To resolve diagnostic and therapeutic problems related to these rare lesions it is essential that their etiopathogenic bases be understood. Auriculobranchial cysts and fistulae present clinical symptoms (cervical, parotid, auricular) that are only poorly evidenced and are related mainly to infection. Surgical excision requires a wide approach route of the parotidectomy type with preliminary isolation of the facial nerve. Thymic cysts result from embryogenic anomalies leading to remnants from the 3rd endobranchial pouch and/or degenerative disorders of Hassal's corpuscles. Of mainly perioperative detection their exeresis requires investigation of possible inferior mediastinal prolongations and preservation of healthy thymic parenchyma. Cystic lymphangiomas arise from dysembryoplasia of the lymphatic system, two opposing pathogenic theories existing to explain their origin. They are serious lesions because of their dissecting tendencies and their inexorable growth in the vast majority of cases. Two forms of lymphangioma, from the embryologic, diagnostic and therapeutic points of view, can be distinguished: those of extraparotid origin and those developing from the parotid.
在儿童中观察到的各种先天性头颈部肿胀中,一般临床实践中很少遇到三种类型:耳颞囊肿和瘘管、胸腺囊肿和囊性淋巴管瘤。为了解决与这些罕见病变相关的诊断和治疗问题,必须了解其病因基础。耳颞囊肿和瘘管的临床症状(颈部、腮腺、耳部)证据不足,主要与感染有关。手术切除需要采用腮腺切除术式的广泛入路,并在术前分离面神经。胸腺囊肿是由胚胎发育异常导致第三鳃囊残余和/或哈氏小体退行性病变引起的。其切除主要在围手术期进行,需要检查是否可能有下纵隔延伸,并保留健康的胸腺实质。囊性淋巴管瘤起源于淋巴系统发育异常,存在两种相反的致病理论来解释其起源。由于其侵袭性倾向和绝大多数病例中不可阻挡的生长,它们是严重的病变。从胚胎学、诊断和治疗角度来看,可区分两种形式的淋巴管瘤:腮腺外起源的和起源于腮腺的。