Money J, Kalus M E
Am J Dis Child. 1979 Aug;133(8):846-50.
The IQ of eight male patients with Noonan's syndrome, aged 13 to 26 years, ranged from 64 to 127, with a median of 102. The full IQ masked the possible presence of specific verbal or praxic (visual-constructional) disability. There was no verbal/praxic disparity in three cases; there was substantial verbal disability in one case; and there was major praxic disability in four cases, three unrelated to vision and one accounted for by severe visual impairment. Ostensible general mental retardation in Noonan's syndrome should always be further evaluated for specific disability. Academic placement should then be arranged accordingly.
8名年龄在13至26岁之间的努南综合征男性患者的智商范围为64至127,中位数为102。整体智商掩盖了可能存在的特定语言或运用障碍(视觉构建方面)。3例患者不存在语言/运用障碍差异;1例存在严重语言障碍;4例存在严重运用障碍,其中3例与视力无关,1例由严重视力损害所致。对于努南综合征表面上的一般性智力迟钝,应始终进一步评估是否存在特定障碍。然后应据此安排学业安置。