多发性内分泌肿瘤综合征

Multiple endocrine neoplasia syndromes.

作者信息

Pont A

出版信息

West J Med. 1980 Apr;132(4):301-12.

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1272066/

Abstract

The multiple endocrine neoplasia (MEN) syndromes consist of three distinct disease entities. They have in common adenomatous, carcinomatous or hyperplastic involvement of a variety of endocrine glands, and an autosomal dominant inheritance. MEN I includes hyperparathyroidism, islet cell and pituitary tumors. The components of MEN IIa are hyperparathyroidism, medullary thyroid carcinoma and pheochromocytoma. MEN IIb includes multiple neuromas, medullary thyroid carcinoma and pheochromocytoma. Effective tests are available for the early detection of components of the syndromes in potentially affected patients. Screening can lead to therapeutic intervention before clinical sequelae ensue.

摘要

多发性内分泌腺瘤病（MEN）综合征由三种不同的疾病实体组成。它们的共同特征是多种内分泌腺出现腺瘤样、癌样或增生性病变，并呈常染色体显性遗传。MEN I包括甲状旁腺功能亢进、胰岛细胞瘤和垂体瘤。MEN IIa的组成部分是甲状旁腺功能亢进、甲状腺髓样癌和嗜铬细胞瘤。MEN IIb包括多发性神经瘤、甲状腺髓样癌和嗜铬细胞瘤。有有效的检测方法可用于早期发现潜在受累患者的综合征组成部分。筛查可在临床后遗症出现之前进行治疗干预。

相似文献

1

Multiple endocrine neoplasia syndromes.

West J Med. 1980 Apr;132(4):301-12.

2

Endocrine tumors.

Vet Clin North Am Small Anim Pract. 1985 May;15(3):643-58. doi: 10.1016/s0195-5616(85)50062-5.

3

Multiple endocrine neoplasia (MEN)--an overview and case report--patient with sporadic bilateral pheochromocytoma, hyperparathyroidism and marfanoid habitus.

Anticancer Res. 2000 Nov-Dec;20(6C):4877-87.

4

The Multiple Endocrine Neoplasia syndromes.

Ann Chir Gynaecol. 1983;72(3):153-9.

5

Multiple endocrine adenomatosis.

Surg Clin North Am. 1974 Apr;54(2):387-93. doi: 10.1016/s0039-6109(16)40286-0.

6

Primary hyperparathyroidism and multiple endocrine neoplasia (MEN).

Endocrinologie. 1982 Jan-Mar;20(1):49-55.

7

Zollinger-Ellison syndrome. An analysis of twenty-five cases.

Am J Surg. 1968 Aug;116(2):293-304. doi: 10.1016/0002-9610(68)90507-2.

8

The importance of multiple endocrine neoplasia syndromes in differential diagnosis.

Klin Wochenschr. 1990 Jul 5;68(13):669-72. doi: 10.1007/BF01667014.

9

Multiple endocrine adenopathy.

Surg Gynecol Obstet. 1983 May;156(5):665-78.

10

Surgical treatment of medullary carcinoma of the thyroid.

Otolaryngol Clin North Am. 1990 Jun;23(3):453-73.

本文引用的文献

1

THE ZOLLINGER-ELLISON SYNDROME: RE-APPRAISAL AND EVALUATION OF 260 REGISTERED CASES.

Ann Surg. 1964 Sep;160(3):512-30. doi: 10.1097/00000658-196409000-00013.

2

PLASMA INSULIN IN ORGANIC HYPERINSULINISM: COMPARATIVE EFFECTS OF TOLBUTAMIDE, LEUCINE AND GLUCOSE.

J Clin Endocrinol Metab. 1964 Aug;24:747-60. doi: 10.1210/jcem-24-8-747.

3

FAMILIAL MULTIPLE ENDOCRINE ADENOMA-PEPTIC ULCER COMPLEX.

Medicine (Baltimore). 1964 Jul;43:481-516.

4

Medullary (solid) carcinoma of the thyroid; a clinicopathologic entity.

J Clin Endocrinol Metab. 1959 Jan;19(1):152-61. doi: 10.1210/jcem-19-1-152.

5

Islet cell tumor and a syndrome of refractory watery diarrhea and hypokalemia.

Am J Med. 1958 Sep;25(3):374-80. doi: 10.1016/0002-9343(58)90075-5.

6

Primary peptic ulcerations of the jejunum associated with islet cell tumors of the pancreas.

Ann Surg. 1955 Oct;142(4):709-23; discussion, 724-8.

7

Pluriglandular adenomatosis of the pituitary, parathyroid and pancreatic islet cells associated with lipomatosis.

J Pathol Bacteriol. 1954 Jul;68(1):225-9. doi: 10.1002/path.1700680127.

8

Genetic aspects of adenomatosis of endocrine glands.

Am J Med. 1954 Mar;16(3):363-71. doi: 10.1016/0002-9343(54)90353-8.

9

Effects of calcium on serum gastrin levels in the zollinger-Ellison syndrome.

N Engl J Med. 1969 Oct 16;281(16):862-6. doi: 10.1056/NEJM196910162811602.

10

The Zollinger-Ellison syndrome with steatorrhea. II. The mechanism of fat and vitamin B 12 malabsorption.

Gastroenterology. 1968 Dec;55(6):705-23.

文献AI研究员

20分钟写一篇综述，助力文献阅读效率提升50倍。

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

文档翻译

学术文献翻译模型，支持多种主流文档格式。