Langer M, Langer R, Friedrich J M
J Mal Vasc. 1982;7(4):317-24.
Basing our observations on a study of 47 cases of angiodysplasia of types F.P. Weber, Klippel-Trénaunay and Servelle-Martorell, we attempted to demonstrate that differentiation of these 3 syndromes is possible if criteria obtained from a non-invasive investigative method are used. This involves taking standard X-rays of the extremities (both sides) which are examined under direct magnification (0.1-01 mm) thus allowing the most exact possible analysis of the skeletal changes. In this way, the Weber syndrome should be suspected if bone prolongation is seen in association with loss of substances from the skeleton. In the Klippel-Trénaunay syndrome, the bone lengthening is not accompanied by bony lesions. In the Servelle-Martorell syndrome bony lesions go hand in hand with limb hypertrophy.
基于对47例F.P. 韦伯型、克-特综合征和塞尔维-马托雷尔综合征血管发育异常病例的研究,我们试图证明,如果使用从非侵入性检查方法获得的标准,这三种综合征是可以区分的。这包括对四肢(双侧)进行标准X线检查,并在直接放大(0.1 - 0.1毫米)下进行观察,从而能够对骨骼变化进行尽可能精确的分析。通过这种方式,如果发现骨骼延长并伴有骨质流失,应怀疑为韦伯综合征。在克-特综合征中,骨骼延长并不伴有骨病变。在塞尔维-马托雷尔综合征中,骨病变与肢体肥大同时存在。