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间性障碍的遗传

Inheritance of intersex disorders.

作者信息

Muram D, Dewhurst J

出版信息

Can Med Assoc J. 1984 Jan 15;130(2):121-5.

Abstract

Intersex disorders result from abnormalities of the sex chromosomes, gonads, internal and external genitalia, sex hormones and gender role. This article reviews the literature on intersex disorders, outlining the characteristics and mode of inheritance, if known, of each. For appropriate and effective management and counselling of patients and their families, physicians must have a good knowledge of the development of the genital tract and of the interaction between genetic sex and environmental influences.

摘要

间性障碍是由性染色体、性腺、内外生殖器、性激素和性别角色异常引起的。本文回顾了有关间性障碍的文献,概述了每种间性障碍(若已知)的特征和遗传模式。为了对患者及其家庭进行恰当有效的管理和咨询,医生必须充分了解生殖道的发育以及遗传性别与环境影响之间的相互作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7110/1875911/794505fbe298/canmedaj01407-0039-a.jpg

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