Cranio-facial and dental anomalies in the Branchio-Skeleto-Genital (BSG) syndrome with suggestions for more appropriate nomenclature.

A Syndrome combining developmental, facial, skeletal, dental and genital abnormalities previously reported as the Branchio-Skeleto-Genital (BSG) Syndrome is discussed and the dental anomalies described more fully. The dentine dysplasia does not fit into the Shield's classification type I or II. The prefix Branchio- is misleading and suggestion is made of a more appropriate nomenclature.