Lessa S, Carreirão S
Ann Plast Surg. 1981 Jun;6(6):482-90. doi: 10.1097/00000637-198106000-00011.
Waardenburg syndrome is characterized by lateral displacement of the medial canthi and lacrimal puncta, a broad nasal root, poliosis, heterochromia iridis, hyperplasia of the medial portion of the eyebrows, and congenital sensorineural deafness. As a group, these symptoms rarely occur in one individual, so care must be taken not to confuse an isolated condition with the syndrome. Of all the manifestations, the authors believe the lateral displacement of the medial canthi is the key factor in making a diagnosis. Sensorineural deafness is the most handicapping symptom. Surgical treatment is indicated for the correction of dystopia canthorum. We present a technique based on a double Z-plasty and nasal transfixion, plus attachment of the medial canthal tendons according to the techniques of Callahan and Mustardé.
瓦登伯革氏综合征的特征为内眦和泪点向外移位、鼻根宽阔、白发症、虹膜异色症、眉内侧部分增生以及先天性感音神经性耳聋。作为一组症状,这些症状很少在一个个体中同时出现,因此必须注意不要将孤立的病症与该综合征混淆。在所有这些表现中,作者认为内眦向外移位是做出诊断的关键因素。感音神经性耳聋是最具致残性的症状。手术治疗适用于矫正内眦异位。我们介绍一种基于双Z成形术和鼻贯穿缝合,并根据卡拉汉和马斯塔德技术附着内眦腱的技术。