Peleg D, Dicker D, Samuel N, Feldberg D, Goldman J A
J Perinat Med. 1983;11(3):179-82.
The antenatal diagnosis of POTTER's Syndrome (bilateral renal agenesis) is important in order to avoid delivery by cesarean section of newborns with congenital anomalies incompatible with life. In seven cases of this syndrome delivered at the Hasharon Hospital, a similar FHR pattern was retrospectively observed in pregnancy and labor suggesting that electronic fetal monitoring (EFM) may possibly contribute to the diagnosis of this condition in utero. Nevertheless, it must be emphasized, that similar cardiotocographic alterations may result from umbilical cord and/or placental compression in the presence of severe oligohydramnios. The latter may, concurrent with POTTER's Syndrome, predispose to changes in intraamniotic pressure transmitted to fetal autonomic centers. Thus, these variations in FHR pattern may be of value only if the presence of other signs of POTTER's Syndrome is confirmed by a reliable ultrasound examination. Further observations of antenatal FHR patterns in a large number of cases of this syndrome may establish their value in the antenatal diagnosis of POTTER's Syndrome.
波特综合征(双侧肾缺如)的产前诊断很重要,这样可以避免剖宫产分娩患有与生命不相容的先天性异常的新生儿。在哈沙龙医院分娩的7例该综合征病例中,回顾性观察到孕期和分娩时类似的胎心率模式,提示电子胎儿监护(EFM)可能有助于宫内诊断这种情况。然而,必须强调的是,在严重羊水过少的情况下,脐带和/或胎盘受压也可能导致类似的胎心监护改变。后者可能与波特综合征同时发生,易使传递至胎儿自主神经中枢的羊膜腔内压力发生变化。因此,只有在通过可靠的超声检查确认存在波特综合征的其他体征时,这些胎心率模式的变化才有价值。对大量该综合征病例的产前胎心率模式进行进一步观察,可能会确定其在波特综合征产前诊断中的价值。