Tewfik T L, Finlayson M, Attia E L
J Otolaryngol. 1981 Feb;10(1):72-7.
Hemangiopericytomas are uncommon soft tissue tumors. While their occurrence in sinuses and soft tissues around the ear is well documented, there are no reports of primary involvement of the temporal bone. This article discusses the case of a 21 year old patient who had a right temporal angioblastic meningioma resected and presented two years later with a hemangiopericytoma that extensively involved the right temporal bone and external auditory canal. In review, the "meningioma" had the same histological features as the auditory tumor and it was evident that both lesions resulted from the growth of a hemangiopericytoma arising from the intracranial aspect of the temporal bone. Electron microscopic examination of the tumor proved useful in making the diagnosis and in evaluating the cytological features that influence prognosis and treatment. Temporal bone involvement was a major problem and the opportunity is taken to document this rare occurrence and to discuss the biological behavior, pathological characteristics, and differential diagnosis of these neoplasms.
血管外皮细胞瘤是一种罕见的软组织肿瘤。虽然其在鼻窦和耳部周围软组织中的发生已有充分记载,但尚无颞骨原发性受累的报道。本文讨论了一名21岁患者的病例,该患者曾切除右颞叶血管母细胞型脑膜瘤,两年后出现广泛累及右颞骨和外耳道的血管外皮细胞瘤。经复查,“脑膜瘤”与耳部肿瘤具有相同的组织学特征,显然这两个病变均源于颞骨颅内面生长的血管外皮细胞瘤。对肿瘤进行电子显微镜检查有助于做出诊断,并评估影响预后和治疗的细胞学特征。颞骨受累是一个主要问题,本文借此记录了这一罕见病例,并讨论了这些肿瘤的生物学行为、病理特征和鉴别诊断。