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刺激敏感性脊髓性肌阵挛

Stimulus-sensitive spinal myoclonus.

作者信息

Davis S M, Murray N M, Diengdoh J V, Galea-Debono A, Kocen R S

出版信息

J Neurol Neurosurg Psychiatry. 1981 Oct;44(10):884-8. doi: 10.1136/jnnp.44.10.884.

DOI:10.1136/jnnp.44.10.884
PMID:7310406
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC491172/
Abstract

Two cases of spinal myoclonus are described; in both patients myoclonus was responsive to stimuli and absent during sleep. The first patient was considered to have viral neuronitis and the condition resolved spontaneously. The second patient had spinal cord ischaemia; there was electro-physiological evidence of abnormal alpha motor neurone activity and histological study of the spinal cord revealed a severe reduction in small and intermediate neurones. This supports the theory that spinal myoclonus may result from abnormal activity of alpha motor neurones released from control by spinal internuncial neurones.

摘要

本文描述了两例脊髓性肌阵挛病例;两名患者的肌阵挛均对刺激有反应,且在睡眠期间消失。首例患者被认为患有病毒性神经炎,病情自行缓解。第二例患者患有脊髓缺血;有α运动神经元活动异常的电生理证据,脊髓组织学研究显示小神经元和中间神经元严重减少。这支持了脊髓性肌阵挛可能由脊髓中间神经元控制释放的α运动神经元异常活动引起的理论。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8a3/491172/a2b05f136502/jnnpsyc00066-0040-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8a3/491172/29f0d13ab18f/jnnpsyc00066-0040-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8a3/491172/a2b05f136502/jnnpsyc00066-0040-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8a3/491172/29f0d13ab18f/jnnpsyc00066-0040-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c8a3/491172/a2b05f136502/jnnpsyc00066-0040-b.jpg

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