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Acquired isolated factor X deficiency associated with systemic amyloidosis. Case report and review of literature.

作者信息

Girmann G, Wilker D, Stadie H, Scheurlen P G

出版信息

Klin Wochenschr. 1980 Sep 1;58(17):859-62. doi: 10.1007/BF01476996.

DOI:10.1007/BF01476996
PMID:7442086
Abstract

The demonstration of acquired isolated factor X deficiency and of a biclonal homogeneous lambda and kappa light polypeptide chain proteinuria in a patient of 49 years having an obscure hepatomegaly gave clinical evidence for the rate, amyloidosis-associated factor X deficiency, which could be proven by postmortem examination. The mechanisms by which amyloid may affect factor X levels in this case may be preferentially binding to the amyloid fibrils of lambda light chain type.

摘要

相似文献

1
Acquired isolated factor X deficiency associated with systemic amyloidosis. Case report and review of literature.
Klin Wochenschr. 1980 Sep 1;58(17):859-62. doi: 10.1007/BF01476996.
2
Systemic amyloidosis associated with factor X deficiency.与X因子缺乏相关的系统性淀粉样变性。
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Spontaneous major bleeding in acquired factor X deficiency secondary to AL-amyloidosis.继发于AL淀粉样变性的获得性因子X缺乏症中的自发性严重出血。
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Cleve Clin J Med. 1987 Sep-Oct;54(5):399-406. doi: 10.3949/ccjm.54.5.399.
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[Factor X deficiency in systemic amyloidosis. Presentation of a case].[系统性淀粉样变性中的因子X缺乏症。1例报告]
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Characterization of amyloid deposits and P component from a patient with factor X deficiency reveals proteins derived from a lambda VI light chain.对一名X因子缺乏症患者的淀粉样沉积物和P成分进行表征,发现其蛋白质来源于λVI轻链。
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Acquired factor X deficiency in light chain amyloidosis: a report of 2 Korean cases.

本文引用的文献

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[ACQUIRED HEMORRHAGIC DIATHESIS CAUSED BY ISOLATED FACTOR X DEFICIENCY].[孤立性因子X缺乏所致获得性出血素质]
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AMYLOIDOSIS ASSOCIATED WITH FACTOR X (STUART) DEFICIENCY; CASE REPORT.与X因子(斯图尔特因子)缺乏相关的淀粉样变性;病例报告。
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Amyloidosis.淀粉样变性
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Unusual haemorrhagic diathesis in atypical primary amyloidosis.非典型原发性淀粉样变性中的异常出血素质
Acta Haematol. 1961 May;25:321-34. doi: 10.1159/000206548.
9
[Hemorrhagic syndrome caused by acquired Stuart-Prower factor deficiency. Amyloidosis. Waldenstrom's disease].[后天性斯图尔特-普罗厄因子缺乏所致出血综合征。淀粉样变性。瓦尔登斯特伦病]
Bull Mem Soc Med Hop Paris. 1966 Jan 14;117(1):41-8.
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[Nephrotic syndrome and acquired deficiency of Stuart factor revealing the presence of amylosis and myeloma].肾病综合征与斯图尔特因子后天缺乏揭示淀粉样变性和骨髓瘤的存在
J Urol Nephrol (Paris). 1972 Sep;78(9):760-4.