Pearl W, Spicer M
South Med J. 1981 Jan;74(1):80-1. doi: 10.1097/00007611-198101000-00028.
We have described a patient with type 4 Ehlers-Danlos syndrome who died of a ruptured pulmonary artery. Of the six subtypes of Ehlers-Danlos syndrome, which can usually be clinically differentiated, only types 1 and 4 appear to be associated with a substantial risk of arterial rupture.
我们描述了一名患有4型埃勒斯-当洛综合征的患者,该患者死于肺动脉破裂。在通常可通过临床进行区分的埃勒斯-当洛综合征的六种亚型中,只有1型和4型似乎与动脉破裂的重大风险相关。