Fisher D, Hiller N
Department of Radiology, Shaare Zedek Medical Center, Jerusalem, Israel.
Clin Radiol. 1994 Mar;49(3):215-6. doi: 10.1016/s0009-9260(05)81782-9.
Cystic lymphangioma is a very rare condition of unknown aetiology. It is generally regarded as a developmental malformation in which obstruction or agenesis of lymphatic tissue results in lymphangiectasia secondary to lack of normal communication of the lymphatic system. Most lymphangiomas occur in the neck (75%) and axillary region (20%). Lymphangiomas may rarely occur in the retroperitoneum, mediastinum, mesentery, omentum, colon, pelvis, groin, spleen, bone and skin. We present a case of multicompartmental tuberculous lymphangioma extending continuously from the superior posterior mediastinum through the retroperitoneum to the right groin, which responded to needle aspiration and antituberculosis drug therapy.
囊性淋巴管瘤是一种病因不明的极为罕见的病症。它通常被视为一种发育畸形，其中淋巴组织的阻塞或发育不全导致淋巴管扩张，继发于淋巴系统缺乏正常连通。大多数淋巴管瘤发生在颈部（75%）和腋窝区域（20%）。淋巴管瘤很少发生在腹膜后、纵隔、肠系膜、网膜、结肠、骨盆、腹股沟、脾脏、骨骼和皮肤。我们报告一例多房性结核性淋巴管瘤病例，该淋巴管瘤从后上纵隔连续延伸至腹膜后，直至右腹股沟，经针吸活检及抗结核药物治疗后病情好转。
