Scheye T, Aufauvre B, Vanneuville G, Vincent G, Goddon R, Dechelotte P
Service de Chirurgie Pédiatrique, Hôtel-Dieu, Clermont-Fd.
J Chir (Paris). 1994 Jan;131(1):27-33.
Cystic lymphangiomas are rarely observed in the abdomen, even in a paediatric surgery ward. From 1977 to 1991, we diagnosed and treated six such lesions in our paediatric surgery department in Clermont-Ferrand. Most of the lymphangiomas were seen in boys. Mesenteric localizations were seen in 4 out of 6 cases with the characteristic chylous contents in 3 cases. There were very many different presenting signs, although two acute episodes of intestinal vuvulus occurred. The clinical features and the usefulness of exploratory techniques are discussed. The frequency of abdominal cystic lymphangiomas is probable underestimated although the number of cases diagnosed will undoubtedly rise with routine echography, especially in the ante-natal period. Surgical exeresis is the standard therapy but other alternative or complementary methods such as sclerosis techniques could be of interest.
囊性淋巴管瘤在腹部很少见,即使在小儿外科病房也是如此。1977年至1991年期间,我们在克莱蒙费朗的小儿外科诊断并治疗了6例此类病变。大多数淋巴管瘤见于男孩。6例中有4例为肠系膜定位,其中3例含有特征性的乳糜样内容物。尽管发生了两例急性肠扭转,但仍有许多不同的表现体征。本文讨论了其临床特征及探查技术的实用性。腹部囊性淋巴管瘤的发生率可能被低估了,不过随着常规超声检查的应用,尤其是在产前检查中,确诊病例数无疑会增加。手术切除是标准治疗方法,但其他替代或辅助方法,如硬化技术,可能也值得关注。