Perez-Atayde A R, Shamberger R C, Kozakewich H W
Department of Pathology, Children's Hospital, Boston, MA 02115.
Am J Surg Pathol. 1993 Jul;17(7):706-14. doi: 10.1097/00000478-199307000-00008.
A 16-year-old female with mediastinal paraganglioma and multicentric gastroduodenal "leiomyoblastomas" was thought to have an incomplete form of the Carney triad. The histologic, ultrastructural, and immunohistochemical findings of the gastroduodenal tumors revealed features of neuroectodermal differentiation. The architecture of the smallest duodenal tumors suggested an origin from the myenteric autonomic ganglia.
一名患有纵隔副神经节瘤和多中心胃十二指肠“平滑肌瘤样肿瘤”的16岁女性被认为患有不完全型卡尼三联征。胃十二指肠肿瘤的组织学、超微结构和免疫组化结果显示出神经外胚层分化的特征。最小的十二指肠肿瘤的结构提示其起源于肌间自主神经节。