Huet R, Bertinchant J P, Nigond J, Stordeur J M, Moragues C, Wittenberg O, Ovtchinnikoff S, Metge L, Lopez F M, Hertault J
Service cardiologie, CHU, Nîmes.
Arch Mal Coeur Vaiss. 1993 Feb;86(2):237-41.
Lipomatous hypertrophy of the interatrial septum is characterised by an accumulation of fatty tissue in the interatrial septum. The authors report three cases, one presenting with sinus tachycardia and the other two being chance findings. Echocardiography associated with cardiac computerised tomography or magnetic resonance imaging usually confirms the diagnosis. In half the cases, supraventricular arrhythmias and suggestive P wave abnormalities are observed on the electrocardiogram. The diagnostic value of transoesophageal echocardiography is emphasised; it demonstrates the massive forms which may obstruct flow from the superior vena cava into the right atrium. The authors observe a discrepancy between the prevalence of this condition in autopsy series (about 1%) and the small number of cases described at echocardiography, suggesting that the diagnosis is probably missed.
房间隔脂肪肥厚的特征是房间隔内脂肪组织堆积。作者报告了3例病例,1例表现为窦性心动过速,另外2例为偶然发现。超声心动图结合心脏计算机断层扫描或磁共振成像通常可确诊。半数病例在心电图上可观察到室上性心律失常和提示性P波异常。强调了经食管超声心动图的诊断价值;它可显示可能阻塞上腔静脉血流进入右心房的巨大形态。作者观察到尸检系列中该疾病的患病率(约1%)与超声心动图描述的病例数较少之间存在差异,提示可能漏诊了该疾病。