治疗后的枫糖尿症中的皮炎。
Dermatitis in treated maple syrup urine disease.
作者信息
Koch S E, Packman S, Koch T K, Williams M L
机构信息
Department of Dermatology, University of California, San Francisco.
出版信息
J Am Acad Dermatol. 1993 Feb;28(2 Pt 2):289-92. doi: 10.1016/0190-9622(93)70036-s.
PMID:8436640
Abstract
Two children who had classic maple syrup urine disease developed an eruptive dermatitis when plasma isoleucine levels, leucine levels, or both fell below normal during periods of protein restriction. The dermatitis was resistant to topical corticosteroid therapy. Rapid resolution occurred after treatment with isoleucine and leucine dietary supplements.
摘要
两名患有典型枫糖尿症的儿童在蛋白质限制期间，当血浆异亮氨酸水平、亮氨酸水平或两者均降至正常水平以下时，出现了爆发性皮疹。这种皮疹对局部皮质类固醇治疗有抵抗性。在补充异亮氨酸和亮氨酸饮食后迅速消退。
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