Chen S C, Peng H C, Chen H C, Chi C S
Department of Pediatric, Veterans General Hospital-Taichung.
Zhonghua Yi Xue Za Zhi (Taipei). 1993 Apr;51(4):314-7.
Cantrell's pentalogy is a congenital anomaly resulting from embryologic development defect. The anomalies observed in this disorder were: (1) a midline, supraumbilical abdominal wall defect, (2) a defect of the lower sternum, (3) a deficiency of the anterior diaphragm, (4) a defect in the diaphragmatic pericardium, (5) congenital intracardiac defects. Its occurrence in the newborn is quite uncommon, though it was first described by Cantrell and his colleagues in 1958. A one-day-old male fullterm newborn was presented. Omphalocele and partial ectopia cordis were noted immediately after birth. Echocardiogram revealed tetralogy of Fallot with atrium septal defect. Operative findings were sternal cleft, pericardial defect and ventral diaphragmatic defect. The literature on clinical manifestations, embryogenic defect and management of Cantrell's pentalogy is reviewed briefly.
坎特雷尔五联症是一种由胚胎发育缺陷导致的先天性异常。该病症中观察到的异常包括：（1）中线脐上腹壁缺损；（2）下胸骨缺损；（3）前膈膜缺损；（4）膈心包缺损；（5）先天性心脏内缺损。尽管它于1958年首次由坎特雷尔及其同事描述，但在新生儿中的发生相当罕见。本文介绍了一名足月出生一天的男婴。出生后立即发现脐膨出和部分心脏异位。超声心动图显示法洛四联症合并房间隔缺损。手术所见为胸骨裂、心包缺损和腹侧膈肌缺损。本文简要回顾了关于坎特雷尔五联症的临床表现、胚胎发育缺陷及治疗的文献。
