[眼咽型肌病：食管上括约肌肌切开术的价值。附1例报告]

[Oculopharyngeal myopathies: value of myotomy of the superior sphincter of the esophagus. Apropos of a case].

作者信息

Vignes S, Lacau Saint Guily J, Colin J Y, Eymard B, Wechsler B, Godeau P

机构信息

Service de médecine interne, hôpital de la Pitié-Salpétrière, Paris, France.

出版信息

Rev Med Interne. 1996;17(12):1017-9. doi: 10.1016/s0248-8663(97)80845-4.

DOI:10.1016/s0248-8663(97)80845-4

PMID:9008749

Abstract

Since 3 years, a 74 year-old man suffered of swallowing impairment, weight loss, bilateral ptosis and proximal muscular weakness. Electron microscopy disclosed intranuclear tubular filaments and confirmed the diagnosis of oculopharyngeal muscular dystrophy. Upper oesophageal sphincter myotomy was performed with complete improvement. Four months after surgery, swallowing disorders were not recurrent and weight gain was substantial.

摘要

3年来，一名74岁男性患有吞咽障碍、体重减轻、双侧上睑下垂和近端肌肉无力。电子显微镜检查发现核内管状细丝，确诊为眼咽型肌营养不良。进行了食管上括约肌肌切开术，症状完全改善。术后4个月，吞咽障碍未复发，体重显著增加。