Jacome D E
Department of Medicine, Franklin Medical Center, Greenfield, Massachusetts, USA.
J Neuroophthalmol. 1997 Jun;17(2):95-100.
The cases of six patients with pronounced, persistent, isolated gaze-evoked orbicularis oculi myokymia (GEOM) discovered fortuitously are described. None had brain-stem lesions, and two had associated, unusual cranial synkinesis (trigeminofacial, hypoglossal-facial, and spinal accessory-facial). Additional features included asymmetric blinking and pseudoblepharoclonus in a third patient and buccopharyngeal synkinesis and post-deglutional tremors in a fourth. Ptosis and pupillary changes were absent. With the possible exception of one case, GEOM seems to be a congenital benign oculofacial synkinesis of brain-stem origin.
本文描述了偶然发现的6例患有明显、持续性、孤立性凝视诱发眼轮匝肌肌纤维颤搐(GEOM)的患者情况。所有患者均无脑干病变,其中2例伴有不寻常的颅神经联合运动(三叉神经-面神经、舌下神经-面神经和副神经-面神经)。其他特征包括,第3例患者存在不对称眨眼和假性眼睑阵挛,第4例患者存在颊咽联合运动和吞咽后震颤。所有患者均无眼睑下垂和瞳孔变化。除1例可能的例外情况外,GEOM似乎是一种源于脑干的先天性良性眼面部联合运动。