McCarthy J F, Hurley J P, Neligan M C, Wood A E
National Cardiac Surgical Unit, Our Lady's Hospital for Sick Children, Crumlin, Dublin, Ireland.
Eur J Cardiothorac Surg. 1997 Jun;11(6):1017-22. doi: 10.1016/s1010-7940(97)01166-4.
Congenital tracheobronchial obstruction (TBO) presents a complex problem both in terms of diverse aetiology, presence of associated anomalies and the operative strategy to be adopted. We report a single centre experience in managing this difficult problem.
Twenty-four infants and children with TBO referred to our unit over a 12-year period are reviewed. Aetiology of TBO included vascular rings (n = 9), anomalous innominate artery (n = 6), congenital tracheal stenosis (n = 5), segmental bronchial stenosis (n = 2) and pulmonary artery compression of the main bronchi (n = 2). Seven patients had concurrent cardiac anomalies. Stridor was the commonest presenting symptom (67%). Mean delay from onset of symptoms to referral was 19 months. One patient died preoperatively due to acute airway obstruction. Mean age at operation was 33.1 +/- 42 months (range 4 days-156 months) and 11 children were under 1 year at the time of surgery. In cases of TBO secondary to vascular rings, division of the ring resulted in relief of symptoms in seven cases, with two requiring further surgery for resultant tracheomalacia. Four of the five patients having tracheal resection were operated on with the use of cardiopulmonary bypass; three of these patients had concurrent correction of cardiac lesions, with two survivors. Tracheobronchial anastomoses were carried out using continuous polydioxanone (PDS). Patients with anomalous innominate arteries required aortopexy in five and innominate artery suspension in one, while those with pulmonary artery compression of the main bronchi had correction of their intracardiac defects (n = 2).
Hospital mortality was 8.7% and there has been one late death due to Eisenmenger syndrome secondary to pulmonary regurgitation, atrial septal defect (ASD) and patent ductus arteriosus (PDA). On follow-up (mean 40 +/- 31 months), 19 patients are alive and symptom free. There have been no anastomotic strictures following tracheobronchial resection. The single most important predictor of mortality was the presence of associated cardiac anomalies.
TBO can be managed effectively by a single operation in both infants and children without a detrimental effect on tracheal growth. We advocate consideration of concurrent repair of the tracheal and cardiac lesions. Cardiopulmonary bypass (CPB) allows this concurrent correction of cardiac lesions and also facilitates tracheal resection.
先天性气管支气管梗阻(TBO)在病因多样性、相关畸形的存在以及所采用的手术策略方面都呈现出复杂的问题。我们报告了在单一中心处理这一难题的经验。
回顾了12年间转诊至我们科室的24例患有TBO的婴幼儿及儿童。TBO的病因包括血管环(n = 9)、无名动脉异常(n = 6)、先天性气管狭窄(n = 5)、节段性支气管狭窄(n = 2)以及主支气管的肺动脉压迫(n = 2)。7例患者合并心脏畸形。喘鸣是最常见的首发症状(67%)。从症状出现到转诊的平均延迟时间为19个月。1例患者术前因急性气道梗阻死亡。手术时的平均年龄为33.1±42个月(范围4天至156个月),11名儿童在手术时年龄小于1岁。在血管环继发的TBO病例中,7例通过切断血管环症状得到缓解,2例因继发气管软化需要进一步手术。5例接受气管切除术的患者中有4例在体外循环下进行手术;其中3例同时矫正了心脏病变,2例存活。气管支气管吻合采用连续聚二氧六环酮(PDS)进行。无名动脉异常的患者中5例行主动脉固定术,1例行无名动脉悬吊术,而主支气管肺动脉压迫的患者中2例矫正了心内缺损。
医院死亡率为8.7%,有一例因肺动脉反流、房间隔缺损(ASD)和动脉导管未闭(PDA)继发艾森曼格综合征导致的晚期死亡。随访(平均40±31个月)时,19例患者存活且无症状。气管支气管切除术后未出现吻合口狭窄。死亡率的唯一最重要预测因素是合并心脏畸形的存在。
TBO在婴幼儿和儿童中均可通过单次手术有效治疗,且对气管生长无不利影响。我们主张考虑同时修复气管和心脏病变。体外循环(CPB)允许同时矫正心脏病变,也便于进行气管切除。