Yang D N, Townsend J C, Ilsen P F, Bright D C, Welton T H
Optemetry Service, West Los Angeles VA Medical Center, California, USA.
J Am Optom Assoc. 1997 Aug;68(8):519-26.
A porencephalic cyst is a cavity within the cerebral hemisphere, filled with cerebrospinal fluid, that communicates directly with the ventricular system. It is a rare condition probably caused by vascular occlusion resulting from an insult during fetal development or an injury occurring later in life. Porencephaly is often associated with various ophthalmic and neurologic signs, including visual-field defects, abnormal pupillary responses, optic nerve hypoplasia, decreased vision, nystagmus, strabismus, hemi-inattention, seizures, and mental deficiencies.
Two cases are presented of patients in whom porencephalic cysts developed as a result of traumatic head injuries. Both had demonstrable visual-field defects, with diagnosis of porencephaly verified by computed tomography scans of the head.
Visual-field defects resulting from porencephalic cysts can mimic those observed with strokes or brain tumors. A thorough case history and complete neurologic workup can assist with differential diagnosis. The clinical features of porencephaly, different theories of brain recovery after trauma, and treatment options are discussed.
脑穿通畸形囊肿是大脑半球内的一个腔隙,充满脑脊液,且与脑室系统直接相通。这是一种罕见病症,可能由胎儿发育期间的损伤或日后生活中发生的损伤导致血管闭塞引起。脑穿通畸形常与各种眼科和神经学体征相关,包括视野缺损、异常瞳孔反应、视神经发育不全、视力下降、眼球震颤、斜视、偏侧忽视、癫痫发作和智力缺陷。
本文介绍了两例因头部外伤而出现脑穿通畸形囊肿的患者。两人均有可证实的视野缺损,头部计算机断层扫描证实了脑穿通畸形的诊断。
脑穿通畸形囊肿导致的视野缺损可能与中风或脑肿瘤所致的视野缺损相似。详尽的病史和全面的神经学检查有助于鉴别诊断。文中讨论了脑穿通畸形的临床特征、创伤后脑恢复的不同理论以及治疗选择。