Werness B A, Guccion J G
The Department of Pathology, The Washington Hospital Center, DC, USA.
Int J Gynecol Pathol. 1997 Jul;16(3):282-5. doi: 10.1097/00004347-199707000-00016.
A rare neoplasm seen in women with von Hippel-Lindau disease is the papillary cystadenoma of the broad ligament, only three cases of which have been reported. All three exhibited characteristic histologic features identical to those of epididymal tumors that occur in affected patients, and were presumed to be of wolffian origin. This is the case of a broad ligament tumor in a woman with von Hippel-Lindau disease that had features more consistent with a mullerian rather than wolffian origin. This is the first report of a broad ligament tumor of probable mullerian origin in von Hippel-Lindau disease.
在患有冯·希佩尔-林道病的女性中可见一种罕见的肿瘤,即阔韧带乳头状囊腺瘤,仅报道过3例。所有3例均表现出与患病患者发生的附睾肿瘤相同的特征性组织学特征,推测起源于中肾管。本文报道1例患有冯·希佩尔-林道病的女性阔韧带肿瘤,其特征更符合苗勒氏起源而非中肾管起源。这是冯·希佩尔-林道病中可能起源于苗勒氏的阔韧带肿瘤的首例报道。