Huang S C, Jiang R, Hufnagle W O, Furst D E, Wilske K R, Milner E C
Department of Immunology, University of Washington, Seattle, USA.
Clin Exp Immunol. 1998 Jun;112(3):516-27. doi: 10.1046/j.1365-2249.1998.00580.x.
The human antibody repertoire has been demonstrated to have a marked V-gene-dependent bias that is conserved between individuals. In RA patients, certain heavy chain V genes (VH) have been found to be preferentially used for encoding autoantibodies. To determine if such preferential use of VH genes in autoantibodies is associated with a general distortion of the V gene repertoire in RA patients, the VH composition of peripheral blood B cells was analysed among four RA patients and four age- and sex-matched healthy controls. Usage of individual VH genes (eight VH3 and three VH4 genes tested by hybridization with a set of gene-specific oligonucleotide probes) was highly biased among RA patients, but no evidence of a distortion in the bias was observed compared with healthy controls. However, the occurrence of somatic mutations in these VH genes (estimated by differential hybridization with motif-specific oligonucleotide probes targeted to CDR and FR of the tested genes, and by DNA sequence analysis) was strikingly different between patients and healthy subjects. The number of VH3 rearrangements that had accumulated somatic mutations and the number of mutations per rearrangement were significantly elevated in three of the four RA patients. A slight but not significant elevation in mutations among rearranged VH4 genes was also observed in these patients. These data suggest that although usage of individual VH genes among peripheral blood B cells is not affected by the disease, the autoimmune process may involve a significant fraction of the B cell compartment.
已证明人类抗体库具有明显的V基因依赖性偏向,且这种偏向在个体之间是保守的。在类风湿关节炎(RA)患者中,已发现某些重链V基因(VH)被优先用于编码自身抗体。为了确定自身抗体中VH基因的这种优先使用是否与RA患者V基因库的总体扭曲有关,对4例RA患者和4例年龄及性别匹配的健康对照者的外周血B细胞的VH组成进行了分析。在RA患者中,单个VH基因的使用(通过与一组基因特异性寡核苷酸探针杂交检测8个VH3基因和3个VH4基因)存在高度偏向,但与健康对照相比,未观察到偏向性扭曲的证据。然而,这些VH基因中体细胞突变的发生率(通过与针对测试基因的互补决定区(CDR)和框架区(FR)的基序特异性寡核苷酸探针进行差异杂交以及DNA序列分析来估计)在患者和健康受试者之间存在显著差异。在4例RA患者中的3例中,积累了体细胞突变的VH3重排数量以及每个重排的突变数量显著升高。在这些患者中,重排的VH4基因中的突变也有轻微但不显著的升高。这些数据表明,虽然外周血B细胞中单个VH基因的使用不受疾病影响,但自身免疫过程可能涉及很大一部分B细胞区室。