Hilker R, Mielke R, Berthold F, Schröder R, Heiss W D
Klinik und Poliklinik für Neurologie, Universität zu Köln.
Nervenarzt. 1998 Jun;69(6):519-24. doi: 10.1007/s001150050307.
Primary intracranial germ cell tumors are rare neurological diseases. Secreting germ cell tumors that predominantly appear in the pineal region are characterized by elevated levels of beta-HCG and AFP in CSF. Adequate diagnostic and therapeutic regimens of these tumors are still under debate. We present the case of a patient suffering from spinal metastasis of a secreting germ cell tumor with raised levels of beta-HCG in CSF. Six years before, a pineocytoma of intermediate differentiation had been diagnosed by stereotaxic biopsy. This demonstrates the importance of an early detection of a germ cell neoplasm in case of midline-sized brain-tumors by evaluation of beta-HCG and AFP in CSF and serum. Today, different therapeutic strategies depending on the histological diagnosis are available and justify a high priority of a surgical tumor biopsy. However, the value of stereotaxic procedures remains controversial. Recently published data gave evidence of a definite improved prognosis of secreting CNS germ cell tumors following combined treatment with high-dose polychemotherapy, surgical resection and radiation of the tumor area. beta-HCG and AFP may serve as useful markers to enable follow-up of the disease.
原发性颅内生殖细胞肿瘤是罕见的神经系统疾病。主要出现在松果体区的分泌性生殖细胞肿瘤的特征是脑脊液中β-HCG和AFP水平升高。这些肿瘤的适当诊断和治疗方案仍在讨论中。我们报告一例患有分泌性生殖细胞肿瘤脊髓转移且脑脊液中β-HCG水平升高的患者。六年前,通过立体定向活检诊断为中度分化的松细胞瘤。这表明对于中线型脑肿瘤患者,通过评估脑脊液和血清中的β-HCG和AFP来早期检测生殖细胞肿瘤的重要性。如今,根据组织学诊断有不同的治疗策略,这证明了手术肿瘤活检具有高度优先性。然而,立体定向手术的价值仍存在争议。最近发表的数据表明,高剂量多药化疗、手术切除和肿瘤区域放疗联合治疗后,分泌性中枢神经系统生殖细胞肿瘤的预后有明显改善。β-HCG和AFP可作为有用的标志物用于疾病的随访。