Thakral C L, Sajwani M J
Department of Pediatric Surgery, Royal Hospital P.O. Box 1331, Postal Code III, Muscat, Sultanate of Oman.
Pediatr Surg Int. 1998 Nov;14(1-2):96-7. doi: 10.1007/s003830050448.
The occurrence of a coexisting congenital diaphragmatic hernia (CDH) and esophageal atresia (EA) with distal tracheoesophageal fistula is extremely rare and is considered highly lethal. Only 19 cases of CDH with EA have been reported in the world literature to date. This is a very challenging clinical problem, and the neonate is likely to deteriorate rapidly. Such a case is reported with a successful outcome, probably the first survivor with a right CDH and EA. Management guidelines for such a case are discussed.
先天性膈疝(CDH)与食管闭锁(EA)合并远端气管食管瘘的情况极为罕见,且被认为具有很高的致死性。迄今为止,世界文献中仅报道了19例CDH合并EA的病例。这是一个极具挑战性的临床问题,新生儿病情可能迅速恶化。本文报道了这样一例获得成功救治的病例,可能是首例患有右侧CDH和EA的幸存者。并讨论了此类病例的管理指南。