Yagmurdur M C, Daphan C, Ozdemir A, Ozenc A, Bayraktar Y, Uzunalimoglu B
Department of General Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey.
Hepatogastroenterology. 1998 Nov-Dec;45(24):2175-8.
The Peutz-Jeghers syndrome is an autosomal dominant inherited disease manifested by a combination of mucocutaneous pigmentation and gastrointestinal hamartomatous polyps that usually cause intussusception and intestinal hemorrhage. We report a case in which the patient has been followed-up on for 14 years and who underwent surgical and endoscopic polyp removal several times as well as one intestinal resection. This time, with the use of combined surgery and perioperative endoscopy, 27 polyps were removed, performing only 3 enterotomies. This is the highest number in one session to be reported in the literature. The usefulness of this technique is providing a "clean small intestine" that allows the patient a longer time interval between laparotomies and reduces the complications associated with multiple laparotomies and resections.
黑斑息肉综合征是一种常染色体显性遗传病，表现为皮肤黏膜色素沉着和胃肠道错构瘤性息肉，常导致肠套叠和肠道出血。我们报告一例患者，已随访14年，多次接受手术和内镜下息肉切除，还进行过一次肠切除术。此次，采用联合手术及围手术期内镜检查，切除了 27 枚息肉，仅进行了 3 次肠切开术。这是文献报道的单次手术切除息肉数量最多的病例。该技术的作用是提供一段“清洁的小肠”，使患者两次剖腹手术之间的间隔时间延长，并减少与多次剖腹手术及切除术相关的并发症。
