Yurdakul Y, Yilmaz M, Demirtürk O S, Miari A, Bilgiç A
Department of Thoracic and Cardiovascular Surgery, Hacettepe University Faculty of Medicine, Ankara.
Turk J Pediatr. 1998 Oct-Dec;40(4):619-25.
A case of truncus arteriosus type II is reported. Truncus arterious is an uncommon congenital cardiac defect where a single great vessel exits the heart. Truncus arteriosus is usually fatal, if untreated. This defect occurs when the conus arteriosus and the truncus divide erroneously in the embryo. Palliative surgery in truncus arteriosus has been unsuccessful. Pulmonary banding has been tried and was ineffective and usually fatal. We operated on a nine-month-old (6200 g) male infant with a type II (Edwards-Collett) defect and a large ventricular septal defect. The pulmonary artery average pressure was 51 mmHg. We performed a cardiopulmonary bypass in the usual manner. Pulmonary arteries were resected from the truncal root, and primary end-to-end anastomosis of the truncal root to the ascending aorta was performed. Right ventricle to pulmonary artery continuity was provided using a valveless Gore-Tex graft. We lost our patient due to intractable pulmonary hypertension on the first postoperative day.
报告了一例II型共同动脉干病例。共同动脉干是一种罕见的先天性心脏缺陷，即单一的大血管从心脏发出。如果不治疗，共同动脉干通常是致命的。这种缺陷发生在胚胎期动脉圆锥和共同动脉干错误分隔时。共同动脉干的姑息性手术一直未成功。尝试过肺动脉环扎术，但无效且通常致命。我们为一名9个月大（6200克）患有II型（爱德华兹-科利特分型）缺陷和大型室间隔缺损的男婴进行了手术。肺动脉平均压为51 mmHg。我们以常规方式进行了体外循环。从共同动脉干根部切除肺动脉，然后将共同动脉干根部与升主动脉进行端端直接吻合。使用无瓣膜的戈尔特斯（Gore-Tex）移植物建立右心室与肺动脉的连续性。患者在术后第一天因顽固性肺动脉高压死亡。
