[肾母细胞瘤与多囊性发育不良肾]

[Nephroblastoma and polycystic dysplastic kidney].

作者信息

Angelone S, La Tella R, De Cesare S, Bianco C, Valentino M L, Martone A

机构信息

U.O. di Chirurgia Pediatrica ad indirizzo Urologico, Azienda Ospedaliera Santobono Pansilipon di Napoli, Italia.

出版信息

Pediatr Med Chir. 1998 Sep-Oct;20(5):333-5.

PMID:10068982

Abstract

The Authors pass on the case of a nephroblastoma, associated to Wilms Tumorlet and combined nephroblastomatosis, arose on a multicystic dysplastic kidney. They examine the relationships between the nephroblastoma and the kidney malformations, the possibility of malignant degeneration of a multicystic dysplastic kidney and the necessity of the nephrectomy as a prevention of the degeneration. At the moment the statistic data don't justify the nephrectomy a the birth to prevent the arising of a nephroblastoma.

摘要

作者介绍了一例发生在多囊性发育不良肾的肾母细胞瘤病例，该病例伴有威尔姆斯瘤栓和合并性肾母细胞瘤病。他们研究了肾母细胞瘤与肾脏畸形之间的关系、多囊性发育不良肾发生恶性退变的可能性以及肾切除术作为预防退变的必要性。目前，统计数据并不支持在出生时进行肾切除术以预防肾母细胞瘤的发生。