Matĕjka T, Hucín B, Marek J, Chaloupecký V, Skovránek J
Dĕtské kardiocentrum FN Motol, Praha.
Rozhl Chir. 1998 Dec;77(12):545-7.
The authors present the case-history of a two-day-old neonate with clinical signs of critical coarctation of the aorta where echocardiography revealed thrombosis of the aortic arch and isthmus. By surgery it was impossible to remove the organized thrombus from the aorta, therefore the portion of the aorta with the thrombus was resected and the aorta was reconstructed by an end-to-end anastomosis. After surgery long-term anticoagulation treatment with Warfarin was started. Examination of haemocoagulation factors, incl. proteins C and S and antithrombin III revealed normal findings. The test for lupus erythematosus was also negative. From the case-history of the mother's pregnancy the cause of the serious congenital aortic thrombosis could not be traced. The child is all right after surgery and thrives.
作者介绍了一名两日龄新生儿的病例史,该新生儿具有主动脉严重缩窄的临床体征,超声心动图显示主动脉弓和峡部有血栓形成。通过手术无法从主动脉中清除机化血栓,因此切除了带有血栓的主动脉部分,并通过端端吻合术重建主动脉。术后开始使用华法林进行长期抗凝治疗。对凝血因子进行检查,包括蛋白C、蛋白S和抗凝血酶III,结果均正常。狼疮检查也呈阴性。从母亲的妊娠病例史中无法追溯到严重先天性主动脉血栓形成的原因。患儿术后情况良好,茁壮成长。