Laude M, Libersa C, mauroy B, Francke J P
Bull Assoc Anat (Nancy). 1976 Mar;60(168):159-66.
The study has been carried out on eight cases of pulmonary atresia with ventricular septal defect, this abnormality involves both valvular atresia and the stenosis of the outflow tract of the right ventricle; that means a pulmonary atresia both valvular and infundibular. The atresia is always combined with a dextroposition of the aorta, overriding the ventricular septum; often with an auricular septal defect or a patency of the foramen ovale. In two cases, other associative caridac malformations exist : either a single ventricle or an atresia of the tricuspid valve. The arterial supply to the lungs may be assured by a persistent duct or by systemic arteries, or an association of both.
该研究针对8例室间隔缺损合并肺动脉闭锁的病例展开,这种异常包括瓣膜闭锁以及右心室流出道狭窄;也就是说,存在瓣膜性和漏斗部的肺动脉闭锁。闭锁总是与主动脉右旋位合并存在,主动脉骑跨于室间隔之上;常伴有房间隔缺损或卵圆孔未闭。在2例病例中,还存在其他相关的心脏畸形:单心室或三尖瓣闭锁。肺部的动脉供血可通过动脉导管未闭或体循环动脉来保证,或者二者同时存在。