Baines D B, Murrell D
Department of Anaesthesia, New Children's Hospital, Royal Alexandra Hospital for Children, Sydney NSW, Australia.
Paediatr Anaesth. 1999;9(2):156-8. doi: 10.1046/j.1460-9592.1999.9220293.x.
The Jervell and Lange-Nielsen syndrome is an autosomal recessive trait characterized by deafness and electrocardiographic changes. These changes include prolongation of the QT interval and T-wave inversion. Treatment may include the use of beta-blockers to prevent the development of malignant ventricular arrhythmias and sudden death. We report a patient with this syndrome, who was receiving propranolol orally and who became hypoglycaemic during the preoperative fasting period prior to cochlear implantation.
杰韦尔和朗格-尼尔森综合征是一种常染色体隐性性状，其特征为耳聋和心电图改变。这些改变包括QT间期延长和T波倒置。治疗可能包括使用β受体阻滞剂以预防恶性室性心律失常和猝死的发生。我们报告了一名患有该综合征的患者，该患者正在口服普萘洛尔，并且在人工耳蜗植入术前的禁食期发生了低血糖。
