Daum R, Zachariou Z
Department of Pediatric Surgery, University of Heidelberg, Germany.
J Pediatr Surg. 1999 Mar;34(3):408-11. doi: 10.1016/s0022-3468(99)90487-6.
The authors discuss six cases of superior and total sternal clefts treated in their department in the last 34 years and discuss the problems of this congenital malformation. The inferior sternal clefts including Cantrell's pentalogy and the total ventral clefts were excluded because in these cases severe associated anomalies require another approach. In superior and total sternal clefts, cardiac, vascular anomalies in lungs and abdomen and craniofacial dysgenesias are rarely present. In these cases a primary repair during the first weeks of life should be performed. Furthermore, the authors describe their own surgical approach, consisting of the conversion of the partial cleft into a total one. Then the rims are trimmed, and a complete approximation of the two segments is possible.
作者讨论了过去34年在他们科室治疗的6例胸骨上段裂和全胸骨裂病例,并探讨了这种先天性畸形的相关问题。不包括胸骨下段裂(包括坎特雷尔五联症)和全腹裂,因为在这些病例中,严重的相关异常需要另一种治疗方法。在胸骨上段裂和全胸骨裂中,心脏、肺和腹部的血管异常以及颅面发育不全很少见。对于这些病例,应在出生后的头几周进行一期修复。此外,作者描述了他们自己的手术方法,包括将部分裂转变为全裂。然后修剪边缘,使两段能够完全对合。