坎特雷尔五联症新生儿完全性胸骨裂的外科治疗

Surgical Management of Total Sternal Cleft in a Pentalogy of Cantrell Neonate.

作者信息

Chong Yooyoung, Gang Mi Hyeon, Choi Ah Young, Chang Mea-Young, Ko Geonil, Yang Hogik, Yu Jae Hyeon

机构信息

Department of Thoracic and Cardiovascular Surgery, Chungnam National University Hospital, Daejeon, Korea.

Department of Pediatrics, Chungnam National University Hospital, Daejeon, Korea.

出版信息

Ann Thorac Surg. 2022 May;113(5):e335-e338. doi: 10.1016/j.athoracsur.2021.07.010. Epub 2021 Jul 29.

DOI:10.1016/j.athoracsur.2021.07.010

PMID:34332997

Abstract

Sternal cleft is a rare malformation with significant morbidity and mortality. It has been associated with other midline fusion defects, most significantly Cantrell's pentalogy, involving the sternum, pericardium, heart, diaphragm, and abdominal wall. This study reported a successfully managed case of a newborn with a total sternal cleft and Cantrell's pentalogy. A review of literature and pertinent management principles was also conducted.

摘要

胸骨裂是一种罕见的畸形，具有较高的发病率和死亡率。它与其他中线融合缺陷有关，最显著的是坎特雷尔五联症，涉及胸骨、心包、心脏、膈肌和腹壁。本研究报告了一例成功治疗的全胸骨裂合并坎特雷尔五联症的新生儿病例。同时还对文献及相关治疗原则进行了综述。