Mugiya S, Suzuki K, Saisu K, Fujita K
Department of Urology, Hamamatsu University School of Medicine, Hamamatsu-shi, Japan.
J Endourol. 1999 Mar;13(2):99-104; discussion 104-6. doi: 10.1089/end.1999.13.99.
We report the first patient who had bilateral pheochromocytoma associated with multiple endocrine neoplasia type 2a syndrome (MEN 2a) and underwent unilateral laparoscopic adrenalectomy followed by contralateral retroperitoneoscopic partial adrenalectomy 2 years later. The postoperative course was uneventful both times, and the patient was cured of hypertension without any need for steroid replacement. Endoscopic partial adrenalectomy is a minimally invasive procedure for pheochromocytoma with mild symptoms. We believe that this procedure has considerable potential for treating bilateral pheochromocytoma, which is frequently observed in patients with MEN 2a.
我们报告了首例患有双侧嗜铬细胞瘤并伴有2a型多发性内分泌肿瘤综合征（MEN 2a）的患者，该患者先接受了单侧腹腔镜肾上腺切除术，两年后又接受了对侧腹膜后腔镜肾上腺部分切除术。两次手术后病程均顺利，患者高血压得以治愈，无需任何类固醇替代治疗。内镜下肾上腺部分切除术是治疗症状较轻的嗜铬细胞瘤的一种微创手术。我们认为该手术在治疗MEN 2a患者中常见的双侧嗜铬细胞瘤方面具有相当大的潜力。
