Küper K D, Stübiger N, Rohrbach J M
Abteilung I (Allgemeine Augenheilkunde mit Poliklinik), Universitäts-Augenklinik Tübingen.
Klin Monbl Augenheilkd. 1999 Mar;214(3):183-4. doi: 10.1055/s-2008-1034773.
We want to present a case of bilateral, unusually large pigment epithelial cysts of the iris.
A four-year old girl presented with multiple, un-usually large, bilateral pigment epithelial iris cysts and tags at the pupillary margin. The right eye additionally presented with two adhesions of the cysts at the corneal endothelium. Otherwise, the anterior and posterior segment as well as the intraocular pressure were normal. The visual acuity was at least 0.8 without glasses, and there was no evidence of strabism or other functional impairments. At normal daylight and with non influenced pupils, the visual axis was not covered by the cysts. Since the lesions anamnesti cally appeared to be congenital and the clinical course had been benign, no therapy was initiated. The patient has been checked on at regular intervalls without any functional or morphological change.
Pigment epithelial cysts of the iris usually do not cause any complications due to their small size and stationary clinical course. In rare cases, the lesions can be so large, that they get into contact with the corneal endothelium and sometimes nearly cause visual impairment by covering the visual axis.
我们想呈现一例双侧虹膜色素上皮囊肿异常增大的病例。
一名4岁女孩，双侧瞳孔边缘有多个异常增大的色素上皮虹膜囊肿及赘生物。右眼另外还有囊肿与角膜内皮的两处粘连。除此之外，眼前节和后节以及眼压均正常。视力在不戴眼镜的情况下至少为0.8，没有斜视或其他功能障碍的迹象。在正常日光下且瞳孔未受影响时，视轴未被囊肿覆盖。由于这些病变在既往史中似乎是先天性的，且临床过程一直是良性的，所以未开始治疗。该患者定期接受检查，未出现任何功能或形态学变化。
虹膜色素上皮囊肿通常因其体积小和临床过程稳定而不会引起任何并发症。在罕见情况下，病变可能会非常大，以至于与角膜内皮接触，有时甚至会因覆盖视轴而几乎导致视力障碍。
