先天性肺囊性腺瘤样畸形合并食管闭锁及气管食管瘘

Congenital cystic adenomatoid malformation of the lung associated with esophageal atresia and tracheoesophageal fistula.

作者信息

De Felice C, Di Maggio G, Messina M, Toti P, Bagnoli F, Bracci R, Tota G

机构信息

Institute of Preventive Pediatrics and Neonatology, University of Siena, Italy.

出版信息

Pediatr Surg Int. 1999;15(3-4):260-3. doi: 10.1007/s003830050571.

DOI:10.1007/s003830050571

PMID:10370039

Abstract

Bronchopulmonary malformations associated with esophageal atresia (EA) and tracheoesophageal fistula (TEF) are extremely rare. The authors describe a case of type II congenital cystic adenomatoid malformation (CCAM) of the right lower lobe associated with EA and TEF (Vogt-Gross type C) in a full-term female infant. The CCAM presented as an incidental radiologic finding, and a contralateral tension pneumothorax developed shortly after surgical repair of the EA. Early recognition of this rare association is essential for correct operative management.

摘要

与食管闭锁（EA）和气管食管瘘（TEF）相关的支气管肺畸形极为罕见。作者描述了一例足月女婴，其右肺下叶存在与EA和TEF（Vogt-Gross C型）相关的II型先天性囊性腺瘤样畸形（CCAM）。该CCAM是偶然通过影像学发现的，在EA手术修复后不久对侧出现张力性气胸。早期识别这种罕见的关联对于正确的手术管理至关重要。